Congenital diaphragmatic hernia is a malformation resulting from incomplete fusion of the pleuroperitoneal membrane, it
occurs in around 1/5000 live newborns, it produces in the vast majority of cases severe symptoms of respiratory failure and
pulmonary arterial hypertension in this age group. Treatment is based on maintaining the best respiratory conditions in the child
through intensive neonatal therapy management and, once this objective is achieved, surgical correction of the anatomical defect
should proceed. Unfortunately, despite the progress in respiratory management of the seriously ill newborn, mortality from this
disease is reported above 75%. We present a case in which the left diaphragmatic hernia associated with pulmonary hypertension
led to a fatal outcome in a newborn, despite timely and adequate interventions.
Keywords: Congenital Diaphragmatic Hernia; Pulmonary Hypertension; Respiratory Failure of The Newborn; Surgical Correction