Anaesthesia Recommendations for Patients
with Loeys-Dietz Syndrome
Volume 1 - Issue 4
Aysun Postaci and İsmail Aytaç*
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- Department of Anesthesiology and Reanimation, Ankara Numune Education and Research Hospital, Turkey
*Corresponding author:
İsmail Aytac, Department of Anesthesiology and Reanimation, Ankara Numune Education and Research Hospital,
Turkey
Received: April 20, 2018; Published: April 26, 2018
DOI: 10.32474/PAPN.2018.01.000116
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Abstract
Loeys-Dietz Syndrome is a otosomal dominant connective tissue disorder which has characteristic triad with
a) Arterial tortuosity, aneurysms or dissections;
b) Hypertelorism; and
c) Bifid uvula or cleft palate.
This review summarizes the features of anesthesia management in this syndrome
Keywords: Loeys-Dietz Syndrome; Anesthesia management
Abbrevations: LDS: Loeys-Dietz Syndrome; TGFBR1: Transforming Growth Factor-Receptor Type 1; ARB: Angiotension Receptor
Blockers; ACE: Angiotension Converting Enzyme
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Introduction|
Anesthesia|
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