Takayasu arteritis is an uncommon chronic arteritis of unknown etiology, which primarily affects large vessels, such as aorta
and its main branches, resulting in ischemia from gradual stenosis of involved arteries. It may also involve the coronary arteries,
and lead to myocardial infarction and sudden death. Misdiagnoses, especially in children is not uncommon. In the present case a
10-year old boy with recently diagnosed retroperitoneal fibrosis and ureteral stenoses died suddenly. In addition to retroperitoneal
fibrosis, with affection of the aorta, the autopsy revealed extensive coronary stenosing, and old myocardial infarctions. The findings
were interpreted as caused by widespread, unknown Takayasu arteritis.