Hemophagocytic lymphohistiocytosis (HLH) is an aggressive and life-threatening syndrome of excessive immune activation. It
commonly affects infants from birth to 18 months of age, but the disease can be seen in children and adults of all ages. HLH can occur as
a familial or sporadic disorder, and it can be triggered by a variety of events that disrupt immune homeostasis. Prompt recognition of the
disease and initiation of treatment is essential for the survival of affected patients ..